Hemifacial hypertrophy abbreviated as (HFH) is rare congenital disease characterized by unilateral enlargement of the head and teeth. It is classified as true. Depending on involvement of soft tissues, teeth, and bones, he further classified hemifacial hypertrophy into (a) true hemifacial hypertrophy and. Two cases of congenital hemifacial hypertrophy are described. To our knowledge , this is the first report of this syndrome in a black African population. Possible.
|Published (Last):||5 October 2016|
|PDF File Size:||6.81 Mb|
|ePub File Size:||7.90 Mb|
|Price:||Free* [*Free Regsitration Required]|
Children with idiopathic hemihypertrophy and Beckwith-Wiedemann syndrome have different constitutional epigenotypes associated with Wilms tumor. Even though there have been sporadic reports of acceptable results[ 2171819 ] following surgical treatment, dearth of literature, the possibility of aggravating the growth, the difficulties in recontouring an entire half of the face, the uncertainties of how much soft tissue reduction should be done and the possibility of suboptimal postoperative esthetics dissuaded us from approaching the condition in an aggressive surgical manner.
All these skeletal features and soft tissue abnormalities were evident in the above case. The patient had deferred treatment until now due to the lack of financial resources.
Congenital Hemifacial Hyperplasia: Clinical Presentation and Literature Review
Dental abnormalities of deciduous teeth are less common and often overlooked. Author information Copyright and License information Disclaimer.
OPG view showed that the mandible was unilaterally enlarged with the body of mandible being longer on the right side with an enlarged right condyle resulting in mandibular deviation to the left [ Figure 5 ]. Three soft growths were present; at the lower labial mucosa, the buccal mucosa, and the retromolar area. Stern, Oral and Maxillofacial Pathology: Peckitt[ 30 ] demonstrated the destabilization of the adipocyte cell membrane following injection of a critical concentration of phosphatidylcholine.
True hemifacial hypertrophy exhibits unilateral enlargement of all tissues, teeth, bones, and soft tissues, characterized by viscerocranial enlargement, bounded by frontal bone superiorly sparing the eyeinferior border of the mandible inferiorly, midline medially, and ear including the pinna laterally.
hypertriphy The prevalence rate of hemifacial hypertrophy is 1: Orofacial soft tissues — Soft tissues around the mouth Actinomycosis Angioedema Basal cell carcinoma Cutaneous sinus of dental origin Cystic hygroma Gnathophyma Ludwig’s angina Macrostomia Melkersson—Rosenthal syndrome Microstomia Noma Oral Crohn’s hypertropny Orofacial granulomatosis Perioral dermatitis Pyostomatitis vegetans.
Skeletal development of cranial bones frontal, parietal, temporal, and skull basezygoma, maxilla, and mandible is accentuated. It was clear that there was a unilateral enhancement of development on this side.
The maxillary and mandibular midline was shifted to the left. The computed tomography showed uniform bony enlargement of the left half of the face including the frontal bone [ Figure 4 ].
OMIM Entry – – HEMIFACIAL HYPERPLASIA
Gesell suggested that the condition may result from a deviation of the normal process of twinning [ 9 ]. The right condyle was found to be irregular and flattened; however, the temporomandibular joint space was maintained. Abstract Hemifacial hyperplasia is a rare congenital malformation characterized by noticeable unilateral excess development of hard and soft tissues of the face.
The tissue surrounding the teeth when compared with the left side hyperteophy enlarged. Rowe[ 8 ] described hypeftrophy in the bemifacial of the abnormal side in three respects; the crown size, the root size and shape, and rate of development. Involvement of upper lip causes displacement of philtrum to the uninvolved side of the face. Temporomandibular jointsmuscles of mastication and malocclusions — Jaw joints, chewing muscles and bite abnormalities Bruxism Condylar resorption Mandibular dislocation Malocclusion Hmeifacial Open bite Overbite Overeruption Overjet Prognathia Retrognathia Scissor bite Maxillary hypoplasia Temporomandibular joint dysfunction.
Deformities of the teeth and their related hard tissues in the jaw are key findings for correct diagnosis, particularly in hemihypertrophy limited to the face.
The patient was well oriented with stable vital signs. Family history was noncontributory. A rare case report.
Procedures are deferred until physiological growth ceases. Bednar’s aphthae Cleft palate High-arched palate Palatal cysts of the newborn Inflammatory papillary hyperplasia Stomatitis nicotina Torus palatinus.
hemufacial Ultrasound assisted liposuction consist of repetitive expansion and passive contraction of adipocytes, resulting in rupture of their cellular membrane and liquefaction of fat. A diverse form of hemifacial hyperplasia.
The patient refused to undergo extensive surgical procedures as the lesion was asymptomatic. Crossed congenital hemifacial hyperplasia.
Case Reports in Dentistry
The patients understand that their names and initials will not be published and due efforts will be made to conceal their identity, but anonymity cannot be guaranteed.